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Differential effects of divalent cations on elk prion protein fibril formation and stability

Misfolding of the normally folded prion protein of mammals (PrP(C)) into infectious fibrils causes a variety of diseases, from scrapie in sheep to chronic wasting disease (CWD) in cervids. The misfolded form of PrP(C), termed PrP(Sc), or in this case PrP(CWD), interacts with PrP(C) to create more Pr...

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Détails bibliographiques
Publié dans:Prion
Auteurs principaux: Samorodnitsky, Daniel, Nicholson, Eric M.
Format: Artigo
Langue:Inglês
Publié: Taylor & Francis 2018
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC5871030/
https://ncbi.nlm.nih.gov/pubmed/29310497
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/19336896.2017.1423187
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