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Deficit in PINK1/PARKIN-mediated mitochondrial autophagy at late stages of dystrophic cardiomyopathy

AIMS: Duchenne muscular dystrophy (DMD) is an inherited devastating muscle disease with severe and often lethal cardiac complications. Emerging evidence suggests that the evolution of the pathology in DMD is accompanied by the accumulation of mitochondria with defective structure and function. Here,...

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Dettagli Bibliografici
Pubblicato in:Cardiovasc Res
Autori principali: Kang, Chifei, Badr, Myriam A, Kyrychenko, Viktoriia, Eskelinen, Eeva-Liisa, Shirokova, Natalia
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5852524/
https://ncbi.nlm.nih.gov/pubmed/29036556
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/cvr/cvx201
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