Import of TAT-Conjugated Propionyl Coenzyme A Carboxylase Using Models of Propionic Acidemia

Eitemau Tebyg

• L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.
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  Cyhoeddwyd: (1984)
• Unequal synthesis and differential degradation of propionyl CoA carboxylase subunits in cells from normal and propionic acidemia patients.
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  Cyhoeddwyd: (1989)
• An unusual insertion/deletion in the gene encoding the beta-subunit of propionyl-CoA carboxylase is a frequent mutation in Caucasian propionic acidemia.
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  Cyhoeddwyd: (1990)
• High Incidence of Propionic Acidemia in Greenland Is Due to a Prevalent Mutation, 1540insCCC, in the Gene for the β-Subunit of Propionyl CoA Carboxylase
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  Cyhoeddwyd: (2000)
• Identification of Propionate as an Endogenous CO(2) Acceptor in Rhodospirillum rubrum and Properties of Purified Propionyl-Coenzyme A Carboxylase
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  Cyhoeddwyd: (1968)