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Lysosomal Acid Lipase Deficiency: Report of Five Cases across the Age Spectrum

Lysosomal acid lipase (LAL) deficiency is an autosomal recessive lysosomal storage disorder caused by mutations in the LIPA gene that leads to premature organ damage and mortality. We present retrospective data from medical records of 5 Brazilian patients, showing the broad clinical spectrum of the...

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Detalles Bibliográficos
Publicado en:Case Rep Pediatr
Main Authors: Curiati, Marco Antonio, Kyosen, Sandra Obikawa, Pereira, Vanessa Gonçalves, Patrício, Francy Reis da Silva, Martins, Ana Maria
Formato: Artigo
Idioma:Inglês
Publicado: Hindawi 2018
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5828415/
https://ncbi.nlm.nih.gov/pubmed/29527374
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2018/4375434
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