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Gradual Symmetric Progression of DFNA34 Hearing Loss Caused by an NLRP3 Mutation and Cochlear Autoinflammation

OBJECTIVE: To characterize the audiometric phenotype of autosomal dominant DFNA34 hearing loss (HL) caused by a missense substitution in the NLRP3 gene. NLRP3 encodes a critical component of the NLRP3 inflammasome that is activated in innate immune responses. STUDY DESIGN: This study was conducted u...

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Bibliografiset tiedot
Julkaisussa:Otol Neurotol
Päätekijät: Nakanishi, Hiroshi, Kawashima, Yoshiyuki, Kurima, Kiyoto, Muskett, Julie A., Kim, H. Jeffrey, Brewer, Carmen C., Griffith, Andrew J.
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: 2018
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC5807171/
https://ncbi.nlm.nih.gov/pubmed/29342053
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MAO.0000000000001715
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