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Activation of the NLRP3 Inflammasome is Associated with Valosin Containing Protein Myopathy

Aberrant activation of the NOD-like receptor (NLR) family, pyrin domain-containing protein 3 (NLRP3) inflammasome triggers a pathogenic inflammatory response in many inherited neurodegenerative disorders. Inflammation has recently been associated with Valosin Containing Protein (VCP)-associated dise...

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Detalhes bibliográficos
Publicado no:Inflammation
Main Authors: Nalbandian, Angèle, Khan, Arif A., Srivastava, Ruchi, Llewellyn, Katrina J., Tan, Baichang, Shukr, Nora, Fazli, Yasmin, Kimonis, Virginia E., BenMohamed, Lbachir
Formato: Artigo
Idioma:Inglês
Publicado em: 2017
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5800525/
https://ncbi.nlm.nih.gov/pubmed/27730320
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10753-016-0449-5
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