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Novel amplification mechanism of prions through disrupting sortilin-mediated trafficking

Conformational conversion of the cellular prion protein, PrP(C), into the abnormally folded isoform of prion protein, PrP(Sc), which leads to marked accumulation of PrP(Sc) in brains, is a key pathogenic event in prion diseases, a group of fatal neurodegenerative disorders caused by prions. However,...

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Библиографические подробности
Опубликовано в: :Prion
Главные авторы: Sakaguchi, Suehiro, Uchiyama, Keiji
Формат: Artigo
Язык:Inglês
Опубликовано: Taylor & Francis 2017
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC5786358/
https://ncbi.nlm.nih.gov/pubmed/29099278
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/19336896.2017.1391435
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