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Dynamic recruitment of ubiquitin to mutant huntingtin inclusion bodies

Many neurodegenerative diseases, such as Huntington’s disease, are hallmarked by the formation of intracellular inclusion bodies (IBs) that are decorated with ubiquitin, proteasomes and chaperones. The apparent enrichment of ubiquitin and components involved in protein quality control at IBs suggest...

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Dettagli Bibliografici
Pubblicato in:Sci Rep
Autori principali: Juenemann, Katrin, Jansen, Anne H. P., van Riel, Luigi, Merkx, Remco, Mulder, Monique P. C., An, Heeseon, Statsyuk, Alexander, Kirstein, Janine, Ovaa, Huib, Reits, Eric A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group UK 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5780509/
https://ncbi.nlm.nih.gov/pubmed/29362455
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-018-19538-0
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