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Novel frameshift mutation in the KCNQ1 gene responsible for Jervell and Lange-Nielsen syndrome

OBJECTIVE(S): Jervell and Lange–Nielsen syndrome is an autosomal recessive disorder caused by mutations in KCNQ1 or KCNE1 genes. The disease is characterized by sensorineural hearing loss and long QT syndrome. MATERIALS AND METHODS: Here we present a 3.5-year-old female patient, an offspring of cons...

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Bibliografski detalji
Izdano u:Iran J Basic Med Sci
Glavni autori: Amirian, Azam, Dalili, Seyed Mohammad, Zafari, Zahra, Saber, Siamak, Karimipoor, Morteza, Akbari, Vahid, Fazelifar, Amir Farjam, Zeinali, Sirous
Format: Artigo
Jezik:Inglês
Izdano: Mashhad University of Medical Sciences 2018
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC5776430/
https://ncbi.nlm.nih.gov/pubmed/29372044
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.22038/IJBMS.2017.23207.5908
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