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The six metal binding domains in human copper transporter, ATP7B: molecular biophysics and disease-causing mutations

Wilson Disease (WD) is a hereditary genetic disorder, which coincides with a dysfunctional copper (Cu) metabolism caused by mutations in ATP7B, a membrane-bound P(1B)-type ATPase responsible for Cu export from hepatic cells. The N-terminal part (~ 600 residues) of the multi-domain 1400-residue ATP7B...

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Dettagli Bibliografici
Pubblicato in:Biometals
Autori principali: Ariöz, Candan, Li, Yaozong, Wittung-Stafshede, Pernilla
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer Netherlands 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5684295/
https://ncbi.nlm.nih.gov/pubmed/29063292
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10534-017-0058-2
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