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TRIM37, a novel E3 ligase for PEX5-mediated peroxisomal matrix protein import

Most proteins destined for the peroxisomal matrix depend on the peroxisomal targeting signals (PTSs), which require the PTS receptor PEX5, whose deficiency causes fatal human peroxisomal biogenesis disorders (PBDs). TRIM37 gene mutations cause muscle–liver–brain–eye (mulibrey) nanism. We found that...

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Detalles Bibliográficos
Publicado en:J Cell Biol
Autores principales: Wang, Wei, Xia, Zhi-Jie, Farré, Jean-Claude, Subramani, Suresh
Formato: Artigo
Lenguaje:Inglês
Publicado: The Rockefeller University Press 2017
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5584156/
https://ncbi.nlm.nih.gov/pubmed/28724525
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.201611170
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