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Striatal Vulnerability in Huntington’s Disease: Neuroprotection Versus Neurotoxicity
Huntington’s disease (HD) is an autosomal dominant neurodegenerative disease caused by the expansion of a CAG trinucleotide repeat encoding an abnormally long polyglutamine tract (PolyQ) in the huntingtin (Htt) protein. In HD, striking neuropathological changes occur in the striatum, including loss...
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| Publicat a: | Brain Sci |
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| Autors principals: | , |
| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
MDPI
2017
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5483636/ https://ncbi.nlm.nih.gov/pubmed/28590448 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/brainsci7060063 |
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