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Striatal Vulnerability in Huntington’s Disease: Neuroprotection Versus Neurotoxicity

Huntington’s disease (HD) is an autosomal dominant neurodegenerative disease caused by the expansion of a CAG trinucleotide repeat encoding an abnormally long polyglutamine tract (PolyQ) in the huntingtin (Htt) protein. In HD, striking neuropathological changes occur in the striatum, including loss...

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Shranjeno v:
Bibliografske podrobnosti
izdano v:Brain Sci
Main Authors: Morigaki, Ryoma, Goto, Satoshi
Format: Artigo
Jezik:Inglês
Izdano: MDPI 2017
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC5483636/
https://ncbi.nlm.nih.gov/pubmed/28590448
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/brainsci7060063
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