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Cystic Fibrosis and the Nervous System

Cystic fibrosis (CF) is a life-shortening autosomal recessive disorder caused by mutations in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR). CFTR is an anion channel that conducts bicarbonate and chloride across cell membranes. Although defective anion transport ac...

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Dades bibliogràfiques
Publicat a:Chest
Autor principal: Reznikov, Leah R.
Format: Artigo
Idioma:Inglês
Publicat: American College of Chest Physicians 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5472519/
https://ncbi.nlm.nih.gov/pubmed/27876591
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.chest.2016.11.009
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