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Brazilian guidelines for the diagnosis and treatment of cystic fibrosis

Cystic fibrosis (CF) is an autosomal recessive genetic disorder characterized by dysfunction of the CFTR gene. It is a multisystem disease that most often affects White individuals. In recent decades, various advances in the diagnosis and treatment of CF have drastically changed the scenario, result...

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Detaylı Bibliyografya
Yayımlandı:J Bras Pneumol
Asıl Yazarlar: Athanazio, Rodrigo Abensur, da Silva, Luiz Vicente Ribeiro Ferreira, Vergara, Alberto Andrade, Ribeiro, Antônio Fernando, Riedi, Carlos Antônio, Procianoy, Elenara da Fonseca Andrade, Adde, Fabíola Villac, Reis, Francisco José Caldeira, Ribeiro, José Dirceu, Torres, Lídia Alice, de Fuccio, Marcelo Bicalho, Epifanio, Matias, Firmida, Mônica de Cássia, Damaceno, Neiva, Ludwig-Neto, Norberto, Maróstica, Paulo José Cauduro, Rached, Samia Zahi, Melo, Suzana Fonseca de Oliveira
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Sociedade Brasileira de Pneumologia e Tisiologia 2017
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC5687954/
https://ncbi.nlm.nih.gov/pubmed/28746534
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/S1806-37562017000000065
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