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Animal and Model Systems for Studying Cystic Fibrosis

The cystic fibrosis (CF) field is the beneficiary of five species of animal models that lack functional cystic fibrosis transmembrane conductance regulator (CFTR) channel. These models are rapidly informing mechanisms of disease pathogenesis and CFTR function regardless of how faithfully a given org...

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Publicat a:J Cyst Fibros
Autors principals: Rosen, Bradley H., Chanson, Marc, Gawenis, Lara R., Liu, Jinghua, Sofoluwe, Aderonke, Zoso, Alice, Engelhardt, John F.
Format: Artigo
Idioma:Inglês
Publicat: 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5828943/
https://ncbi.nlm.nih.gov/pubmed/28939349
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jcf.2017.09.001
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