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Prion Protein Regulates Iron Transport by Functioning as a Ferrireductase

Prion protein (PrP(C)) is implicated in the pathogenesis of prion disorders, but its normal function is unclear. We demonstrate that PrP(C) is a ferrireductase (FR), and its absence causes systemic iron deficiency in PrP knock-out mice (PrP(−/−)). When exposed to non-transferrin-bound (NTB) radioact...

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Dettagli Bibliografici
Pubblicato in:J Alzheimers Dis
Autori principali: Singh, Ajay, Haldar, Swati, Horback, Katharine, Tom, Cynthia, Zhou, Lan, Meyerson, Howard, Singh, Neena
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5450724/
https://ncbi.nlm.nih.gov/pubmed/23478311
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/JAD-130218
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