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Impaired novelty acquisition and synaptic plasticity in congenital hyperammonemia caused by hepatic glutamine synthetase deficiency

Genetic defects in ammonia metabolism can produce irreversible damage of the developing CNS causing an impairment of cognitive and motor functions. We investigated alterations in behavior, synaptic plasticity and gene expression in the hippocampus and dorsal striatum of transgenic mice with systemic...

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Publicat a:Sci Rep
Autors principals: Chepkova, Aisa N., Sergeeva, Olga A., Görg, Boris, Haas, Helmut L., Klöcker, Nikolaj, Häussinger, Dieter
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5220341/
https://ncbi.nlm.nih.gov/pubmed/28067279
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep40190
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