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Cockayne syndrome: Clinical features, model systems and pathways

Cockayne syndrome (CS) is a disorder characterized by a variety of clinical features including cachectic dwarfism, severe neurological manifestations including microcephaly and cognitive deficits, pigmentary retinopathy, cataracts, sensorineural deafness, and ambulatory and feeding difficulties, lea...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:Ageing Res Rev
Prif Awduron: Karikkineth, Ajoy C., Scheibye-Knudsen, Morten, Fivenson, Elayne, Croteau, Deborah L., Bohr, Vilhelm A.
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: 2016
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC5195851/
https://ncbi.nlm.nih.gov/pubmed/27507608
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.arr.2016.08.002
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