Cargando...

Amyloid fibrils from the N-terminal prion protein fragment are infectious

Recombinant C-terminally truncated prion protein PrP23-144 (which corresponds to the Y145Stop PrP variant associated with a Gerstmann–Sträussler–Scheinker-like prion disease) spontaneously forms amyloid fibrils with a parallel in-register β-sheet architecture and β-sheet core mapping to residues ∼11...

Descripción completa

Guardado en:
Detalles Bibliográficos
Publicado en:Proc Natl Acad Sci U S A
Autores principales: Choi, Jin-Kyu, Cali, Ignazio, Surewicz, Krystyna, Kong, Qingzhong, Gambetti, Pierluigi, Surewicz, Witold K.
Formato: Artigo
Lenguaje:Inglês
Publicado: National Academy of Sciences 2016
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5137684/
https://ncbi.nlm.nih.gov/pubmed/27849581
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1610716113
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!