In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR.

Lignende værker

• Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation
  af: Stefano, Daniela De, et al.
  Udgivet: (2014)
• The potentiator ivacaftor is essential for pharmacological restoration of F508del-CFTR function and mucociliary clearance in cystic fibrosis
  af: Anita Balázs, et al.
  Udgivet: (2025-05-01)
• Potentiator Ivacaftor Abrogates Pharmacological Correction of ΔF508 CFTR in Cystic Fibrosis
  af: Cholon, Deborah M., et al.
  Udgivet: (2014)
• The holy grail of cystic fibrosis research: pharmacological repair of the F508del-CFTR mutation
  af: Maiuri, Luigi, et al.
  Udgivet: (2015)
• Chloride channel and chloride conductance regulator domains of CFTR, the cystic fibrosis transmembrane conductance regulator
  af: Schwiebert, Erik M., et al.
  Udgivet: (1998)