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Glycation in Demetalated Superoxide Dismutase 1 Prevents Amyloid Aggregation and Produces Cytotoxic Ages Adducts

Superoxide dismutase 1 (SOD1) has been implicated with familial amyotrophic lateral sclerosis (fALS) through accumulation of protein amyloid aggregates in motor neurons of patients. Amyloid aggregates and protein inclusions are a common pathological feature of many neurological disorders in which pr...

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Pubblicato in:Front Mol Biosci
Autori principali: Sirangelo, Ivana, Vella, Filomena M., Irace, Gaetano, Manco, Giuseppe, Iannuzzi, Clara
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5026054/
https://ncbi.nlm.nih.gov/pubmed/27695694
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fmolb.2016.00055
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