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Marfanoid–progeroid–lipodystrophy syndrome: a newly recognized fibrillinopathy

We review six previous reports between 2000 and 2014 of seven unrelated patients with mutations in the FBN1 gene affecting function. All mutations occurred in exon 64 of the FBN1 gene. A distinctive phenotype consisting of partial manifestations of Marfan syndrome, a progeroid facial appearance, and...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Eur J Hum Genet
Egile Nagusiak: Passarge, Eberhard, Robinson, Peter N, Graul-Neumann, Luitgard M
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Nature Publishing Group 2016
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4989216/
https://ncbi.nlm.nih.gov/pubmed/26860060
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/ejhg.2016.6
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