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DNAH11 Localization in the Proximal Region of Respiratory Cilia Defines Distinct Outer Dynein Arm Complexes
Primary ciliary dyskinesia (PCD) is a recessively inherited disease that leads to chronic respiratory disorders owing to impaired mucociliary clearance. Conventional transmission electron microscopy (TEM) is a diagnostic standard to identify ultrastructural defects in respiratory cilia but is not us...
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| Publicado en: | Am J Respir Cell Mol Biol |
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| Autores principales: | , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , |
| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
American Thoracic Society
2016
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC4979367/ https://ncbi.nlm.nih.gov/pubmed/26909801 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1165/rcmb.2015-0353OC |
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