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DNAH11 Localization in the Proximal Region of Respiratory Cilia Defines Distinct Outer Dynein Arm Complexes

Primary ciliary dyskinesia (PCD) is a recessively inherited disease that leads to chronic respiratory disorders owing to impaired mucociliary clearance. Conventional transmission electron microscopy (TEM) is a diagnostic standard to identify ultrastructural defects in respiratory cilia but is not us...

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Publicat a:Am J Respir Cell Mol Biol
Autors principals: Dougherty, Gerard W., Loges, Niki T., Klinkenbusch, Judith A., Olbrich, Heike, Pennekamp, Petra, Menchen, Tabea, Raidt, Johanna, Wallmeier, Julia, Werner, Claudius, Westermann, Cordula, Ruckert, Christian, Mirra, Virginia, Hjeij, Rim, Memari, Yasin, Durbin, Richard, Kolb-Kokocinski, Anja, Praveen, Kavita, Kashef, Mohammad A., Kashef, Sara, Eghtedari, Fardin, Häffner, Karsten, Valmari, Pekka, Baktai, György, Aviram, Micha, Bentur, Lea, Amirav, Israel, Davis, Erica E., Katsanis, Nicholas, Brueckner, Martina, Shaposhnykov, Artem, Pigino, Gaia, Dworniczak, Bernd, Omran, Heymut
Format: Artigo
Idioma:Inglês
Publicat: American Thoracic Society 2016
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4979367/
https://ncbi.nlm.nih.gov/pubmed/26909801
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1165/rcmb.2015-0353OC
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