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Severe muscle wasting and denervation in mice lacking the RNA-binding protein ZFP106

Innervation of skeletal muscle by motor neurons occurs through the neuromuscular junction, a cholinergic synapse essential for normal muscle growth and function. Defects in nerve–muscle signaling cause a variety of neuromuscular disorders with features of ataxia, paralysis, skeletal muscle wasting,...

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Detalles Bibliográficos
Publicado en:Proc Natl Acad Sci U S A
Main Authors: Anderson, Douglas M., Cannavino, Jessica, Li, Hui, Anderson, Kelly M., Nelson, Benjamin R., McAnally, John, Bezprozvannaya, Svetlana, Liu, Yun, Lin, Weichun, Liu, Ning, Bassel-Duby, Rhonda, Olson, Eric N.
Formato: Artigo
Idioma:Inglês
Publicado: National Academy of Sciences 2016
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4978283/
https://ncbi.nlm.nih.gov/pubmed/27418600
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1608423113
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