Loading...

Efficacy of lumacaftor-ivacaftor for the treatment of cystic fibrosis patients homozygous for the F508del-CFTR mutation

Cystic fibrosis (CF) results from mutations in the CF transmembrane conductance regulator (CFTR) gene, which codes for the CFTR channel protein. The most common mutation in CF is F508del, which produces a misfolded protein with diminished channel activity. The development of small-molecule CFTR-modu...

Fuld beskrivelse

Na minha lista:
Bibliografiske detaljer
Udgivet i:Expert Rev Precis Med Drug Dev
Main Authors: Cholon, Deborah M., Esther, Charles R., Gentzsch, Martina
Format: Artigo
Sprog:Inglês
Udgivet: 2016
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC4963025/
https://ncbi.nlm.nih.gov/pubmed/27482545
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/23808993.2016.1175299
Tags: Tilføj Tag
Ingen Tags, Vær først til at tagge denne postø!