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Insights into Mucopolysaccharidosis I from the structure and action of α-L-Iduronidase

Mucopolysaccharidosis type I (MPS I), caused by mutations in the gene encoding α-L-iduronidase (IDUA), is one of approximately 70 genetic disorders collectively known as the lysosomal storage diseases. To gain insight into the basis for MPS I, we have crystallized human IDUA produced in an Arabidops...

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Bibliografski detalji
Izdano u:Nat Chem Biol
Glavni autori: Bie, Haiying, Yin, Jiang, He, Xu, Kermode, Allison R., Goddard-Borger, Ethan D., Withers, Stephen G., James, Michael N. G.
Format: Artigo
Jezik:Inglês
Izdano: 2013
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4954775/
https://ncbi.nlm.nih.gov/pubmed/24036510
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/nchembio.1357
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