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Evaluation of α‐iduronidase in dried blood spots is an accurate tool for mucopolysaccharidosis I diagnosis

Background: Mucopolysaccharidosis type I (MPS I) is caused by a deficiency of the α‐l‐iduronidase (IDUA), which leads to the accumulation of glycosaminoglycans in lysosomes. MPS I patients present a spectrum ranging from a severe to an attenuated phenotype. Once clinical suspicion is present, diagno...

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Detalles Bibliográficos
Publicado en:J Clin Lab Anal
Main Authors: Müller, Karen B., Pereira, Vanessa G., Martins, Ana M., D'Almeida, Vânia
Formato: Artigo
Idioma:Inglês
Publicado: Wiley Subscription Services, Inc., A Wiley Company 2011
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6647646/
https://ncbi.nlm.nih.gov/pubmed/21786328
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jcla.20468
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