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Molecular mousetraps, α(1)-antitrypsin deficiency and the serpinopathies

Point mutations in members of the serine proteinase inhibitor or serpin superfamily cause them to change shape, polymerise and be deposited in the tissues. This process is best seen in mutants of α(1)-antitrypsin within hepatocytes to cause periodic acid-Schiff (PAS) positive inclusions and cirrhosi...

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Detalles Bibliográficos
Publicado en:Clin Med (Lond)
Autor Principal: Lomas, David A
Formato: Artigo
Idioma:Inglês
Publicado: Royal College of Physicians 2005
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4952210/
https://ncbi.nlm.nih.gov/pubmed/16011217
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.7861/clinmedicine.5-3-249
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