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α(1)-Antitrypsin deficiency • 4: Molecular pathophysiology

The molecular basis of α(1)-antitrypsin deficiency is reviewed and is shown to be due to the accumulation of mutant protein as ordered polymers within the endoplasmic reticulum of hepatocytes. The current goals are to determine the cellular response to polymeric α(1)-antitrypsin and to develop thera...

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Detalhes bibliográficos
Main Authors: Lomas, D, Parfrey, H
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Group 2004
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1747018/
https://ncbi.nlm.nih.gov/pubmed/15170041
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/thx.2003.006528
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