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In situ characterization of protein aggregates in human tissues affected by light chain amyloidosis: a FTIR microspectroscopy study

Light chain (AL) amyloidosis, caused by deposition of amyloidogenic immunoglobulin light chains (LCs), is the most common systemic form in industrialized countries. Still open questions, and premises for developing targeted therapies, concern the mechanisms of amyloid formation in vivo and the bases...

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Dettagli Bibliografici
Pubblicato in:Sci Rep
Autori principali: Ami, Diletta, Lavatelli, Francesca, Rognoni, Paola, Palladini, Giovanni, Raimondi, Sara, Giorgetti, Sofia, Monti, Luca, Doglia, Silvia Maria, Natalello, Antonino, Merlini, Giampaolo
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4931462/
https://ncbi.nlm.nih.gov/pubmed/27373200
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep29096
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