Carregant...

7-dehydrocholesterol efficiently supports Ret signaling in a mouse model of Smith-Opitz-Lemli syndrome

Smith-Lemli-Opitz syndrome (SLOS) is a rare disorder of cholesterol synthesis. Affected individuals exhibit growth failure, intellectual disability and a broad spectrum of developmental malformations. Among them, renal agenesis or hypoplasia, decreased innervation of the gut, and ptosis are consiste...

Descripció completa

Guardat en:
Dades bibliogràfiques
Publicat a:Sci Rep
Autors principals: Gou-Fàbregas, Myriam, Macià, Anna, Anerillas, Carlos, Vaquero, Marta, Jové, Mariona, Jain, Sanjay, Ribera, Joan, Encinas, Mario
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4917867/
https://ncbi.nlm.nih.gov/pubmed/27334845
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep28534
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!