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Cohesin and Human Disease

Cornelia de Lange syndrome (CdLS) is a dominant multisystem disorder caused by a disruption of cohesin function. The cohesin ring complex is composed of four protein subunits and more than 25 additional proteins involved in its regulation. The discovery that this complex also has a fundamental role...

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Pubblicato in:Annu Rev Genomics Hum Genet
Autori principali: Liu, Jinglan, Krantz, Ian D.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2008
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4894839/
https://ncbi.nlm.nih.gov/pubmed/18767966
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1146/annurev.genom.9.081307.164211
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