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Familial vasculitides: granulomatosis with polyangitis and microscopic polyangitis in two brothers with differing anti-neutrophil cytoplasm antibody specificity

Anti-neutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV) is a group of rare autoimmune diseases. Although the aetiology of AAV is uncertain, it is likely that genetic and environmental factors contribute. We report the unusual case of two brothers presenting with AAV with differing clin...

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Publicado en:Clin Kidney J
Autores principales: Prendecki, Maria, Cairns, Tom, Pusey, Charles D.
Formato: Artigo
Lenguaje:Inglês
Publicado: Oxford University Press 2016
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4886912/
https://ncbi.nlm.nih.gov/pubmed/27274829
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/ckj/sfw016
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