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Familial vasculitides: granulomatosis with polyangitis and microscopic polyangitis in two brothers with differing anti-neutrophil cytoplasm antibody specificity

Anti-neutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV) is a group of rare autoimmune diseases. Although the aetiology of AAV is uncertain, it is likely that genetic and environmental factors contribute. We report the unusual case of two brothers presenting with AAV with differing clin...

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Detalhes bibliográficos
Publicado no:Clin Kidney J
Main Authors: Prendecki, Maria, Cairns, Tom, Pusey, Charles D.
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4886912/
https://ncbi.nlm.nih.gov/pubmed/27274829
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/ckj/sfw016
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