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Familial vasculitides: granulomatosis with polyangitis and microscopic polyangitis in two brothers with differing anti-neutrophil cytoplasm antibody specificity

Anti-neutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV) is a group of rare autoimmune diseases. Although the aetiology of AAV is uncertain, it is likely that genetic and environmental factors contribute. We report the unusual case of two brothers presenting with AAV with differing clin...

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Pubblicato in:Clin Kidney J
Autori principali: Prendecki, Maria, Cairns, Tom, Pusey, Charles D.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4886912/
https://ncbi.nlm.nih.gov/pubmed/27274829
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/ckj/sfw016
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