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Elastase levels and activity are increased in dystrophic muscle and impair myoblast cell survival, proliferation and differentiation

In Duchenne muscular dystrophy, progressive loss of muscle tissue is accompanied by fibrosis, chronic inflammation and reduced muscle regenerative capacity. Although much is known about the development of fibrosis and chronic inflammation in muscular dystrophy, less is known about how they are mecha...

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Detalhes bibliográficos
Publicado no:Sci Rep
Main Authors: Arecco, N., Clarke, C. J., Jones, F. K., Simpson, D. M., Mason, D., Beynon, R. J., Pisconti, A.
Formato: Artigo
Idioma:Inglês
Publicado em: Nature Publishing Group 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4886533/
https://ncbi.nlm.nih.gov/pubmed/27241590
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep24708
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