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Pulmonary arterial hypertension in primary amyloidosis

Abstract. Amyloidosis involves extravascular deposition of fibrillar proteins within tissues and organs. Primary light chain amyloidosis represents the most common form of systemic amyloidosis involving deposition of monoclonal immunoglobulin light chains. Although pulmonary amyloid deposition is co...

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Publicado en:Pulm Circ
Autores principales: Cirulis, Meghan M., Emerson, Lyska L., Bull, David A., Hatton, Nathan, Nativi-Nicolai, Jose, Hildebrandt, Gerhard C., Ryan, John J.
Formato: Artigo
Lenguaje:Inglês
Publicado: University of Chicago Press 2016
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4869930/
https://ncbi.nlm.nih.gov/pubmed/27252852
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1086/686172
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