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Pulmonary arterial hypertension in primary amyloidosis
Abstract. Amyloidosis involves extravascular deposition of fibrillar proteins within tissues and organs. Primary light chain amyloidosis represents the most common form of systemic amyloidosis involving deposition of monoclonal immunoglobulin light chains. Although pulmonary amyloid deposition is co...
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| Pubblicato in: | Pulm Circ |
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| Autori principali: | , , , , , , |
| Natura: | Artigo |
| Lingua: | Inglês |
| Pubblicazione: |
University of Chicago Press
2016
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| Soggetti: | |
| Accesso online: | https://ncbi.nlm.nih.gov/pmc/articles/PMC4869930/ https://ncbi.nlm.nih.gov/pubmed/27252852 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1086/686172 |
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