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Bone morphogenetic protein signalling in heritable versus idiopathic pulmonary hypertension

Mutations in gene encoding for bone morphogenetic protein type 2 receptor (BMPR-2) have been reported in pulmonary arterial hypertension (PAH), but their functional relevance remains incompletely understood. BMP receptors expression was evaluated in human lungs and in cultured pulmonary artery smoot...

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Dettagli Bibliografici
Pubblicato in:Eur Respir J
Autori principali: Dewachter, Laurence, Adnot, Serge, Guignabert, Christophe, Tu, Ly, Marcos, Elisabeth, Fadel, Elie, Humbert, Marc, Dartevelle, Philippe, Simonneau, Gérald, Naeije, Robert, Eddahibi, Saadia
Natura: Artigo
Lingua:Inglês
Pubblicazione: European Respiratory Society 2009
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4838637/
https://ncbi.nlm.nih.gov/pubmed/19324947
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1183/09031936.00183008
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