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Atypical MR lenticular signal change in infantile isovaleric acidemia

Isovaleric acidemia (IVA) is an inborn error of branched chain amino acid metabolism that may manifest as acute neonatal metabolic acidosis or as chronic intermittent form with developmental delay or recurrent episodes of acute metabolic acidosis. Early diagnosis is the key to prevent morbidity and...

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Détails bibliographiques
Publié dans:Indian J Radiol Imaging
Auteurs principaux: Wani, Nisar A, Qureshi, Umer Amin, Jehangir, Majid, Ahmad, Kaiser, Hussain, Zahid
Format: Artigo
Langue:Inglês
Publié: Medknow Publications & Media Pvt Ltd 2016
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4813063/
https://ncbi.nlm.nih.gov/pubmed/27081237
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/0971-3026.178362
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