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Atypical MR lenticular signal change in infantile isovaleric acidemia

Isovaleric acidemia (IVA) is an inborn error of branched chain amino acid metabolism that may manifest as acute neonatal metabolic acidosis or as chronic intermittent form with developmental delay or recurrent episodes of acute metabolic acidosis. Early diagnosis is the key to prevent morbidity and...

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Detalhes bibliográficos
Publicado no:Indian J Radiol Imaging
Main Authors: Wani, Nisar A, Qureshi, Umer Amin, Jehangir, Majid, Ahmad, Kaiser, Hussain, Zahid
Formato: Artigo
Idioma:Inglês
Publicado em: Medknow Publications & Media Pvt Ltd 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4813063/
https://ncbi.nlm.nih.gov/pubmed/27081237
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/0971-3026.178362
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