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Differing Microdeletion Sizes and Breakpoints in Chromosome 7q11.23 in Williams-Beuren Syndrome Detected by Chromosomal Microarray Analysis

Williams-Beuren syndrome (WBS) manifests as supravalvular aortic stenosis, intellectual disability, developmental delay and characteristic facial features. The common WBS deletion region ranges from 1.55 to 1.84 Mb and primarily contains the ELN gene. We analyzed 10 patients diagnosed with 7q11.23 m...

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Detalhes bibliográficos
Publicado no:Mol Syndromol
Main Authors: Li, Lin, Huang, Linhuan, Luo, Yanmin, Huang, Xuan, Lin, Shaobin, Fang, Qun
Formato: Artigo
Idioma:Inglês
Publicado em: S. Karger AG 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4802981/
https://ncbi.nlm.nih.gov/pubmed/27022327
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000443942
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