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Acquired von Willebrand syndrome: von Willebrand factor propeptide to von Willebrand factor antigen ratio predicts remission status

We investigated a case of acquired von Willebrand syndrome (AVWS) secondary to a nonneutralizing anti-von Willebrand factor (VWF) antibody associated with an autoimmune disorder. At diagnosis, VWF activity (VWF:Act), antigen (VWF:Ag), multimers, and factor VIII coagulant activity were virtually abse...

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Detalhes bibliográficos
Publicado no:Blood
Main Authors: Lee, Adrienne, Sinclair, Gary, Valentine, Karen, James, Paula, Poon, Man-Chiu
Formato: Artigo
Idioma:Inglês
Publicado em: American Society of Hematology 2014
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4729537/
https://ncbi.nlm.nih.gov/pubmed/24951428
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood-2014-02-557132
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