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Baseline Analysis of a Young Alpha-1-AT Deficiency Liver Disease Cohort Reveals Frequent Portal Hypertension

OBJECTIVE: Alpha-1-antitrypsin deficiency (A1AT) is a common genetic disease with unpredictable and highly variable course. The Childhood Liver Disease Research and Education Network (ChiLDREN) is an NIH, multi-center, longitudinal consortium studying pediatric liver diseases, with the objective of...

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Publicado en:J Pediatr Gastroenterol Nutr
Autores principales: Teckman, Jeffrey H, Rosenthal, Philip, Abel, Robert, Bass, Lee M., Michail, Sonia, Murray, Karen F., Rudnick, David A., Thomas, Daniel W., Spino, Cathie, Arnon, Ronen, Hertel, Paula M., Heubi, James, Kamath, Binita M., Karnsakul, Wikrom, Loomes, Kathleen M., Magee, John C., Molleston, Jean P., Romero, Rene, Shneider, Benjamin L, Sherker, Averell H, Sokol, Ronald J
Formato: Artigo
Lenguaje:Inglês
Publicado: 2015
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4692167/
https://ncbi.nlm.nih.gov/pubmed/25651489
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MPG.0000000000000753
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