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Distributions of Globotriaosylceramide Isoforms, and Globotriaosylsphingosine and Its Analogues in an α-Galactosidase A Knockout Mouse, a Model of Fabry Disease

Fabry disease is caused by deficient activity of α-galactosidase A (GLA) and characterized by systemic accumulation of glycosphingolipids, substrates of the enzyme. To gain insight into the pathogenesis of Fabry disease based on accumulated substrates, we examined the tissue and plasma distributions...

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Detalhes bibliográficos
Publicado no:PLoS One
Main Authors: Sueoka, Hideaki, Aoki, Mikio, Tsukimura, Takahiro, Togawa, Tadayasu, Sakuraba, Hitoshi
Formato: Artigo
Idioma:Inglês
Publicado em: Public Library of Science 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4685999/
https://ncbi.nlm.nih.gov/pubmed/26661087
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0144958
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