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Monogenic forms of childhood obesity due to mutations in the leptin gene

Congenital leptin deficiency is a rare autosomal recessive monogenic obesity syndrome caused by mutations in the leptin gene. This review describes the molecular and cellular characteristics of the eight distinct mutations found so far in humans.

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Publicado en:Mol Cell Pediatr
Autores principales: Funcke, Jan-Bernd, von Schnurbein, Julia, Lennerz, Belinda, Lahr, Georgia, Debatin, Klaus-Michael, Fischer-Posovszky, Pamela, Wabitsch, Martin
Formato: Artigo
Lenguaje:Inglês
Publicado: Springer Berlin Heidelberg 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4644131/
https://ncbi.nlm.nih.gov/pubmed/26567097
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s40348-014-0003-1
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