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Differential allelic expression of SOS1 and hyperexpression of the activating SOS1 c.755C variant in a Noonan syndrome family

Noonan syndrome (NS) is a genetic condition characterized by congenital heart defects, short stature and characteristic facial features. We here present the case of a girl with moderate learning disabilities, delayed language development, craniofacial features and skin anomalies reminiscent of NS. A...

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Detalhes bibliográficos
Publicado no:Eur J Hum Genet
Main Authors: Moncini, Silvia, Bonati, Maria Teresa, Morella, Ilaria, Ferrari, Luca, Brambilla, Riccardo, Riva, Paola
Formato: Artigo
Idioma:Inglês
Publicado em: Nature Publishing Group 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4613488/
https://ncbi.nlm.nih.gov/pubmed/25712082
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/ejhg.2015.20
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