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Investigating heart-specific toxicity of amyloidogenic immunoglobulin light chains: A lesson from C. elegans

Abnormalities in protein folding are involved in many localized and systemic diseases, all of which are characterized by insoluble amyloid formation and deposition. In immunoglobulin light chain (LC) amyloidosis, the most frequent systemic form of amyloidosis, the amyloid involvement of the heart di...

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Detalles Bibliográficos
Publicado en:Worm
Autores principales: Diomede, Luisa, Rognoni, Paola, Lavatelli, Francesca, Romeo, Margherita, di Fonzo, Andrea, Foray, Claudia, Fiordaliso, Fabio, Palladini, Giovanni, Valentini, Veronica, Perfetti, Vittorio, Salmona, Mario, Merlini, Giampaolo
Formato: Artigo
Lenguaje:Inglês
Publicado: Taylor & Francis 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4588172/
https://ncbi.nlm.nih.gov/pubmed/26430549
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4161/21624046.2014.965590
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